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1:18
YouTube
JAMA Network
Tremor and Myoclonus Due To Action Myoclonus Renal Failure Syndrome (AMRFS)
A 22 year old women presented with a bilateral jerky tremor, stimulus-sensitive myoclonus, difficulty with tandem gait, and rapidly progressive renal failure with nephrotic-range proteinuria. Renal biopsy demonstrated focal segmental glomerulosclerosis (FSGS). The video shows postural and action tremor of her outstretched hands, with myoclonus ...
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